Non-Trigger Anesthesia Management in a Patient With Leigh's Syndrome Presenting for Dental Rehabilitation.

Mark McIntosh,'s picture
PubMed URL: 
http://www.ncbi.nlm.nih.gov/pubmed/26705519
Author: 
Siddiqu MS
Author List: 
Suleman MI
Edala T
Abraham E
Siddiqu MS
Journal: 
Anesth Pain Med
PubMed ID: 
26705519
Pagination: 
e28804
Volume: 
5
Issue: 
6
Abstract: 
Usually presenting in infancy, Leigh's syndrome is an inherited condition often manifesting with seizures, ataxia, developmental delay, and dysarthria. The disorder is rare, appearing in approximately 1 in 40,000 live births. Consequently, providing these patients with a suitable plan by which to administer anesthetics remains problematic.We report a male patient with Leigh's syndrome and a family history suggestive of unknown hypotonia and malignant hyperthermia presenting for dental rehabilitation.Dexmedetomidine with remifentanil can be used with no complication in this senerio.
Published Date: 
December, 2015

Bradley L. Schlaggar, M.D., Ph.D., Named President and CEO of Kennedy Krieger Institute

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