Oromaxillofacial osseous abnormality in Sturge-Weber syndrome: case report and review of the literature.

Mark McIntosh,'s picture
PubMed URL: 
http://www.ncbi.nlm.nih.gov/pubmed/16484391
Author: 
Comi AM
Author List: 
Lin DD
Gailloud P
McCarthy EF
Comi AM
Journal: 
AJNR Am J Neuroradiol
PubMed ID: 
16484391
Pagination: 
274-7
Volume: 
27
Issue: 
2
Abstract: 
We report a case of a 17-month-old child affected by Sturge-Weber syndrome who had unusually rapid overgrowth of the left frontal, temporal, orbital, and maxillary regions. CT angiography illustrated osteohypertrophy with periostitis and associated soft tissue hypertrophy directly corresponding to the distribution of the cutaneous port-wine stain. Extended maxillectomy was performed because of rapid growth and clinical debilitation, with surgical pathology revealing juvenile ossifying fibroma.
Published Date: 
February, 2006

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