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Cervical spinal stenosis in metatropic dysplasia.
|Title||Cervical spinal stenosis in metatropic dysplasia.|
|Publication Type||Journal Article|
|Year of Publication||2006|
|Authors||Leet AI, Sampath JS, Scott CI, MacKenzie WG|
|Journal||Journal of pediatric orthopedics|
|Date Published||2006 May-Jun|
Metatropic dysplasia is a rare skeletal dysplasia characterized by rapid collapse of the thoracolumbar spine into kyphoscoliosis. Other spinal anomalies associated with metatropic dysplasia include odontoid hypoplasia and atlantoaxial instability leading to cervical myelopathy. Children with metatropic dysplasia evaluated at our institution for spinal deformity showed evidence of cervical stenosis with or without associated cord compression. Magnetic resonance imaging was found to demonstrate these changes. The association of cervical spinal stenosis and metatropic dysplasia has not been previously described. This has significant treatment implications, because decompression over the stenotic segments should be considered in conjunction with spinal fusion for treatment of odontoid hypoplasia or atlantoaxial instability. A retrospective review of 13 cases of metatropic dysplasia was performed. Despite the challenges provided by this patient population, the chance to halt or reverse neurological dysfunction and improve deformity necessitates prompt surgical intervention.
|Alternate Journal||J Pediatr Orthop|